Ariunaa congenital spine disorders

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1. Abnormalities of NeurulationAnomalies of Notochord DevelopmentAnomalies of Vertebral Formation and SegmentationNormal Anatomical VariationsCongenital and Developmental AbnormalitiesAnomalies of the Caudal Cell Mass

2. :

Spinal dysraphism . Caudal spinal anomalies .

OPEN SPINAL DYSRAPHISM 99% myelomeningoceles OSD Chiari II .

Spina bifida aperta:MYELOCELE AND MYELOMENINGOCELE .

Spina bifida occulta:

Spina bifida aperta: Meningocele Myelomeningocele Myelocystocele lipomeningocele

Posterior meningocele.A, Sagittal T1-weighted MR 12 B, Sagittal T2-weighted MR 5 C, Sagittal T2-weighted MR .

Meningocele.T2 - 6 .

Thoracic Meningocele.

Chiaric-I malformation: - syrinx . Tonsil foramen magnum- 5- Chairi I . 5 Tonsil ectopia . MRI: Peg-like . V sergeant stripes sign . 3- .I: II: III: syrinx

Chiari -1 Malformation.

Chiari Type 1 Malformation.

Chiari-II malformation: myelomeningocele. . Low-lying torcular herophili - , tectal beaking , , .

Fetal T2-weighted MR images. A, Chiari II malformation ( arrows ) on sagittal image. B, Lumbosacral myelocele with low-placed spinal cord ( arrow ) on axial image. C, Dysraphic defect plus placode ( arrow) on axial image.

Chiari II malformation ( arrows in A ) and lumbosacral myelomeningocele ( arrow in B ) on sagittal T2-weighted fetal MR images.

Chiari Type 11 Malformation.

Type II Chiari malformation in a 14-month-old child. Sagittal T1-weighted images demonstrating hydrocephalus (A) with a small posterior fossa and downward herniation of the cerebellum and medulla (B).

Chiari-III malformation:

ccipital encephalocele . Syringomyelia hydrocephalus .

Chiari- IV malformation: .

Type 3 Chiari malformation.

Chiari III.

Type IV Chiari malformation.

Type IV Chiari malformation.

Spinal Dysraphisms : intradural lipoma, filar lipoma, tight filum terminale, persistent terminal ventricle dermal sinus . .

Epidermoid / Dermoid.

2 . , .MRI:

T1: hyperintenseT2: hypointenseT1 C+ (Gd): no enhancement : hypointense

Neurenteric cyst in 3-year-old girl.A and B, Sagittal T2-weighted (A) and axial T1-weighted (B) MR images show bilobed neurenteric cyst (arrows) extending from central canal into posterior mediastinum.C, Three-dimensional CT reconstruction image shows osseous opening (arrow) through which neurenteric cyst passes. This opening is called the Kovalevsky canal.

- Spina bifida spinous process/ lamina . 1-TH1 .A dermal sinus , .

Dermal sinus.A and B, Sagittal schematic (A) and sagittal T2-weighted MR image (B) in 9-year-old girl show intradural dermoid (stars) with tract extending from central canal to skin surface (black arrows). Note tenting of dural sac at origin of dermal sinus (white arrows). C, Axial T2-weighted MR image from same patient as in B shows posterior location of hyperintense dermoid (arrow).

Thoracic dermal sinus ( black arrows ) and dermoid cyst ( white arrows ) on sagittal T1-weighted ( A ), sagittal T2-weighted ( B ), and axial T1-weighted ( C ) MR images.

Thoracic dermal sinus ( posterior black and white arrows in A, and B ) and cyst with enhancing abscess ( anterior white arrows in B ) with cord edema on sagittal T2-weighted ( A ) and gadolinium-enhanced T1- weighted ( B ) MR images.

Disorders of midline notochordal integration: Diastematomyelia 2 . 2 . . 1- . 2- 2 .

Type 1 diastematomyelia.AC, Sagittal T2-weighted MR (A), axial T2-weighted MR (B), and axial CT with bone algorithm (C) images in 6-year-old boy show two dural tubes separated by osseous bridge (arrows), which is characteristic for type 1 diastematomyelia.

Lumbar diastematomyelia and split cord with two hemicords ( short arrows in A and B ), two dural sacs, and a bony septum ( long arrows in B and C ) on axial T2-weighted MR images ( A and B ) and an axial CT scan ( C ).

Type 2 diastematomyelia.AC, Sagittal T1-weighted (A), coronal T1-weighted (B), and axial T2-weighted (C) MR images in 9-year-old girl show splitting of distal cord into two hemicords (whitearrows, B and C) within single dural tube, which is characteristic for type 2 diastematomyelia. Incidental filum lipoma (black arrows, A and B) is present as well.

Lumbar diastematomyelia with tethered hemicords ( long arrows ), no septum, and a lipoma ( short arrow ) on sagittal T1-weighted ( A ) and axial T2-weighted ( B ) MR images.

Asomia L2 .

Left hemivertebra- T11 ..

Butterfly vertebra - .

Butterfly vertebra.

Block vertebra. L3-L4 (block vertebra).

Dorsal hemivertebra .oronal clefts

Hemi-vertebrae & Segmented Vertebrae.

: butterfly vertebra, hemivertebra, tripedicular vertebra, butterfly vertebra.

Limbus vertebra. 4- .

limbus vertebra.

Teardrop . Teardrop .

40 . L5 .Sacralisation of L5 vertebra.

Spondylodysplasias:Spondylodysplasia , , , Scheuermann

Neurofibromatosis.Achondroplasia.Mucopolysaccharidoses.Down syndrome.Spondyloepiphyseal dysplasia.Craniocervical anomalies.Klippel-Feil syndrome.Spinal vascular anomalies.

Idiopathic Scoliosis . 10- . , 2 . , , , .Congenital scoliosis and kyphosis - block vertebrae, hemivertebra, butterfly vertebra .

Idiopathic scoliosis

1, 2 , hemivertebrae hydrosyringomyelia coronal T2-weighted MR . Hemivertebrae .

Scheuermann Diseasesteochondrodysplasia, Scheuermann . , , , .

Scheuermann disease .

Occipitalization of the atlas

Occipitalization of the Atlas

Atlas assimilation tlanto-occipital fusion

, , .C1C2 C2C3 30- .

Atlas assimilation a. (zone 1 assimilation). b. (zone 2 assimilation). . (zone 3) assimilation.

tlanto-occipital fusion

Occipital vertebrae

Epitransverse Processes Paracondylar, Paramastoid processes

Vertebralization of the Atlas . 2 2 1 . (occipitalization), (vertebralization) . .The odontoid process .

Klippel-Feil Anomaly and Syndrome:

The Klippel-Feil anomaly . , , Klippel-Feil . Sprengel- (omovertebral bone) .

Thank You.